Nadir AM Ali, Fathilah Jaais, S Chandrasekhara Reddy
Department of Ophthalmology, Faculty of Medicine, University of Malaya, Kuala Lumpur, Malaysia

Ocular involvement of incontinentia pigmenti is rare in Asian patients. This report is of a 17-year-old Chinese girl who was diagnosed with incontinentia pigmenti in infancy. She has ocular, skin, and dental manifestations of incontinentia pigmenti. At the last follow-up, her vision in the right eye was no light perception and her best-corrected vision in the left eye was 6/6. Fluorescein fundus angiography of the left eye showed leakage within the macula and ischaemic areas in the peripheral retina for which laser photocoagulation was done. She continues to be followed up.

Key words: Cataract, Incontinentia pigmenti, Retinal detachment, Vitreoretinopathy, proliferative

Asian J Ophthalmol. 2007;9:179-181.